Ovarian Rhabdomyosarcoma: Alveolar RMS (PAX3/7–FOXO1 fusion–associated subset)

Last reviewed: 9/15/2025

Summary

An ultra-rare ovarian sarcoma with skeletal-muscle differentiation. Management borrows from soft-tissue/rhabdomyosarcoma playbooks plus ovary-specific surgical principles.

Pathology & Markers

Biology & Pathways

Clinical Challenges

Imaging Notes

Related

Educational use only; not medical advice.